Pulmonary arteriovenous malformation as a cause of exercise intolerance in children: a case report

  • Pierluigi Morreale
  • Veronica Notarbartolo Università degli Studi di Palermo
  • Giancarlo Allegro
  • Mario Giuseppe Vallone
  • Francesca Finazzo
  • Vincenzo Antona
  • Maria Fiorella Sanfilippo
  • Calogero Comparato
Keywords: pulmonary arteriovenous malformation; exercise intolerance; oxygen desaturation; case-report

Abstract

Pulmonary arteriovenous malformations (PAVMs) in children are rare lesions characterized by abnormal low resistance vascular structures connecting a pulmonary artery to a pulmonary vein, resulting in an intrapulmonary right-to-left shunt. The insidious onset and variable signs and symptoms make diagnosis difficult, especially in children. PAVMs can be single or multiple, congenital or acquired, and up to 47-80% of cases are associated with hereditary hemorrhagic telangiectasia (HHT).

References

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Published
2023-06-27
How to Cite
1.
Morreale P, Notarbartolo V, Allegro G, Vallone M, Finazzo F, Antona V, Sanfilippo M, Comparato C. Pulmonary arteriovenous malformation as a cause of exercise intolerance in children: a case report. PI [Internet]. 27Jun.2023 [cited 12Nov.2024];63(3):208-2. Available from: https://www.paediatricaindonesiana.org/index.php/paediatrica-indonesiana/article/view/2637
Section
Case Report
Received 2021-03-31
Accepted 2023-06-27
Published 2023-06-27