Metastatic pancreatic ductal adenocarcinoma in a teenage girl: A rare disease

Metastatic pancreatic ductal adenocarcinoma

  • Sutaryo Sutaryo
  • Scolastika Dita Kristian Department of Child Health, Faculty of Medicine, Public Health and Nursing, Universitas Gadjah Mada - Dr. Sardjito General Hospital, Yogyakarta
Keywords: pancreatic ductal adenocarcinoma; pediatric

Abstract

Pancreatic ductal adenocarcinoma (PDAC) is highly uncommon in patients < 20 years of age, at less than 0.1% of population.1 Pancreatic tumors in children and adolescents can develop from endocrine or exocrine cells. The tumor types include solid pseudopapillary tumor, ductal adenocarcinoma, pancreatoblastoma, acinar cell carcinoma, and pancreatic endocrine neoplasm (malignant and benign).2 Other types of tumors may be attached to it or secondarily engage the gland or emerge from other kinds of non-pancreatic cells inside the pancreas. The prevalent type of classic PDAC in adults is highly uncommon in children.  We report here on a fifteen-year old girl with metastatic pancreatic ductal adenocarcinoma (mPDAC), who presented with abdominal discomfort and jaundice.

References

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Published
2020-11-13
How to Cite
1.
Sutaryo S, Kristian S. Metastatic pancreatic ductal adenocarcinoma in a teenage girl: A rare disease. PI [Internet]. 13Nov.2020 [cited 3Dec.2024];60(6):341-. Available from: https://www.paediatricaindonesiana.org/index.php/paediatrica-indonesiana/article/view/2276
Section
Pediatric Hemato-Oncology
Received 2019-08-20
Accepted 2020-11-13
Published 2020-11-13