Metastatic pancreatic ductal adenocarcinoma in a teenage girl: A rare disease Metastatic pancreatic ductal adenocarcinoma

Main Article Content

Sutaryo Sutaryo
Scolastika Dita Kristian

Abstract

Pancreatic ductal adenocarcinoma (PDAC) is highly uncommon in patients < 20 years of age, at less than 0.1% of population.1 Pancreatic tumors in children and adolescents can develop from endocrine or exocrine cells. The tumor types include solid pseudopapillary tumor, ductal adenocarcinoma, pancreatoblastoma, acinar cell carcinoma, and pancreatic endocrine neoplasm (malignant and benign).2 Other types of tumors may be attached to it or secondarily engage the gland or emerge from other kinds of non-pancreatic cells inside the pancreas. The prevalent type of classic PDAC in adults is highly uncommon in children.  We report here on a fifteen-year old girl with metastatic pancreatic ductal adenocarcinoma (mPDAC), who presented with abdominal discomfort and jaundice.

Article Details

How to Cite
1.
Sutaryo S, Kristian S. Metastatic pancreatic ductal adenocarcinoma in a teenage girl: A rare disease. PI [Internet]. 13Nov.2020 [cited 3Mar.2021];60(6). Available from: https://www.paediatricaindonesiana.org/index.php/paediatrica-indonesiana/article/view/2276
Section
Pediatric Hemato-Oncology
Received 2019-08-20
Accepted 2020-11-13
Published 2020-11-13

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